Symptoms of Incontinentia Pigmenti

General information about symptoms of Incontinentia Pigmenti: The symptom information on this page attempts to provide a list of some possible symptoms of Incontinentia Pigmenti. This symptom information has been gathered from various sources, may not be fully accurate, and may not be the full list of symptoms of Incontinentia Pigmenti. Furthermore, symptoms of Incontinentia Pigmenti may vary on an individual basis for each patient. Only your doctor can provide adequate diagnosis of symptoms and whether they are indeed symptoms of Incontinentia Pigmenti.

List of symptoms of Incontinentia Pigmenti: The list of symptoms mentioned in various sources for Incontinentia Pigmenti includes:

Stage 1 symptoms:
- Skin redness
- Spiral lines of small fluid-filled blisters
Stage 2 symptoms:
- Warty skin growths - on arms or legs or sometimes head or torso; often follow the same pattern as Stage 1 blisters
Stage 3 symptoms:
- Skin discolorations
Stage 4 symptoms:
- Reduced pigmentation
Other less common symptoms:

Symptoms of Incontinentia Pigmenti: IP is divided into 4 stages, which frequently overlap or appear together. During the first stage, which begins between birth and 6 months of age, there is inflammation accompanied by skin redness and spiral lines of small fluid-filled blisters. The second stage gradually develops with rough, warty skin growths which appear on the arms or legs and, sometimes, on the head or trunk. These growths, which are often arranged in the same spiral or linear pattern as in the first stage, usually resolve during infancy or early childhood. The third stage begins between 3 months and 2 years of age and is characterized by discolorations appearing in unusual patterns. The fourth stage consists of diminished pigmentation or atrophy in areas of previous discoloration. In rare cases of IP, hair loss with scarring and non-dermatological symptoms such as dental problems (delayed tooth growth or decay, missing or malformed teeth), diminished vision, seizures, muscle spasms, or slight paralysis may occur. Developmental abnormalities including dwarfism or short stature, club foot, spina bifida, skull and ear deformities, cleft lip or palate, atrophy on one side of the body, abnormal development of cartilage, congenital dislocation of hip, incomplete development of one side of the spinal bones, and extra ribs or webbed fingers may occur with the disorder but are not characteristic. In a few cases of IP, extremely wooly or kinky hair and an immune system dysfunction may also appear. ¹

More symptoms of Incontinentia Pigmenti: In addition to the above information, to get a full picture of the possible symptoms of this condition and its related conditions, it may be necessary to examine symptoms that may be caused by complications of Incontinentia Pigmenti, underlying causes of Incontinentia Pigmenti, associated conditions for Incontinentia Pigmenti, risk factors for Incontinentia Pigmenti, or other related conditions.

Medical articles on symptoms: These general reference articles may be of interest:

Footnotes:
1. excerpt from NINDS Incontinentia Pigmenti Information Page: NINDS

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